Darnis F, Fauvert RMésothéliome péritonéal malin diffus (ascite visqueuse Quinton A, Beylot J, Lebras MPéritonites gélatineuses (à propos de 2 cas). Dec 18, The main sign is abdominal ascites: from a simple effusion to an . La maladie gélatineuse du péritoine à propos d’un cas: médecine du. Jun 6, Request PDF on ResearchGate | La maladie gélatineuse du péritoine | Pseudomyxoma peritonei or gelatinous ascites is a rare clinical entity.
|Published (Last):||3 September 2016|
|PDF File Size:||1.33 Mb|
|ePub File Size:||18.8 Mb|
|Price:||Free* [*Free Regsitration Required]|
There was a problem providing the content you requested
Other less common signs include abdominal pain, weight loss, urinary symptoms, constipation, vomiting, and dyspnea. The final pathological result allows to determine the TNM classification and the stage of the disease. Computed tomography and sonography. Differential diagnosis The differential diagnosis includes secondary peritoneal carcinomatoses gelatienuse other rare peritoneal tumors.
Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. Ovarian and peritoneal biopsies are performed.
Ann Surg Ann Surg Oncol 4 All results will be presented to the tumor board to decide on further treatment. Moreover, no current imaging can visualize peritoneal lesions in preoperative and postoperative surgery.
The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. The peritoneal lavage is then carried out. It is a mucinous neoplasia of low grade, with or without cysts, characterized by a proliferation of cylindrical epithelial cells, planar or villous architecture without mucus, neoplastic cells, and invasive extraappendicular focus.
Diagnostic There are no specific signs.
Orphanet: Maladie gelatineuse du peritoine
Molecular genetic evidence supporting the clonality and appendiceal origin of pseudomyxoma peritonei in women. The surgery must obligatorily remove the appendix, sometimes even a right hemicolectomy and hysterectomy with bilateral adnexectomy.
Summary and related texts.
Giant mucocele of the appendix. Abstract The authors report a case of pseudomyxoma peritonei with gelatinous peritoneum in a year-old-woman. So we need of a starting rate. Tumor blood markers are ineffective and do not evaluate response to treatment. In fact, intraoperative chemotherapy 8 — 11 and postoperative chemotherapy significantly improve the prognosis.
Thoracoabdominal contrast-enhanced MRI and CT scan were then performed after an endovaginal ultrasound showing a left adnexal ovarian mass that is heterogeneous and little mobile. The diagnosis is based on chest-abdominal-pelvic computed tomography CAP-CT findings revealing the characteristic compartmentalized distribution pattern of mucinous ascites and on pathology performed by two expertswhile tumor markers carcinoembryonic antigen and CA are relatively non-specific.
A written informed consent was obtained from the patient for the publication of this case report. Epithelial tumors Non-epithelial tumors Adenoma: J Clin Oncol There are no specific signs. Mucinous Cystadenomas Gelxtineuse is a mucinous neoplasia of low grade, with or without cysts, characterized by a proliferation of cylindrical epithelial cells, planar or villous architecture without mucus, neoplastic cells, and invasive extraappendicular focus.
The gelatinous substance is often associated with a malignant ovarian tumor or appendicitis perforated.
Elias D, Sabourin JC. This article was submitted to Visceral Surgery, a section of the journal Frontiers in Surgery. Ann Surg Oncol 15 5: Imaging findings of urachal mucinous cystadenocarcinoma associated with pseudomyxoma peritonei.
The laparoscopy allows the exploration of peritoneal cavity and defines a peritoneal carcinoma index. Check this box if you wish to receive a copy acsite your message.
There are currently no validated recommendations on clinical management and no cytotoxic agents have been granted a European Marketing Authorization MA in this indication. The results of this review are in contradiction with the MRI. A complementary ultrasound is performed, which shows heterogeneous fluid mass that do not move around the left ovary, without mobilization to the right during the right lateral decubitus.