Darnis F, Fauvert RMésothéliome péritonéal malin diffus (ascite visqueuse Quinton A, Beylot J, Lebras MPéritonites gélatineuses (à propos de 2 cas). Dec 18, The main sign is abdominal ascites: from a simple effusion to an . La maladie gélatineuse du péritoine à propos d’un cas: médecine du. Jun 6, Request PDF on ResearchGate | La maladie gélatineuse du péritoine | Pseudomyxoma peritonei or gelatinous ascites is a rare clinical entity.

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The surgery must obligatorily remove the appendix, sometimes even a right hemicolectomy and hysterectomy with bilateral adnexectomy. Immunohistochemistry and genetics history were to be expected to affect the appendicular mucocele as the main cause of the disease.

Orphanet: Maladie gelatineuse du peritoine

Group 3 consists of lesions of mucinous neoplasia of low grade, with or without cysts, characterized by a proliferation of cylindrical epithelial cells, flat or villous architecture with the presence of mucus, extraappendicular neoplastic cells, and absence of invasive extraappendicular focus.

Journal page Archives Sommaire.

But, ascihe main problem is the posttraumatic and post-surgical scarring, explaining imperatively a surgical and chemotherapeutic management at the same time.

Intraperitoneal chemotherapy of peritoneal carcinomatosis using pressurized aerosol as an alternative toliquid solution: In fact, intraoperative chemotherapy 8 — 11 and postoperative chemotherapy significantly improve the prognosis. Am J Surg Pathol 30 Werth on described a gelatinous subperitoneal cavity due to the rupture of a pseudo awcite ovarian cyst with a gelatinous material but without mucine 1.


TNM classification for mucinous peritoneal tumor: The mucocele is due to the chronic nature of luminal distension. Specialised Social Services Eurordis directory.

Pseudomyxome péritonéal

Access to the text HTML. No other abnormalities are found in the abdominal cavity.

Its base showed a mucocele of 1. The final pathological result allows to determine the TNM classification and the stage of the disease. But the absence of pathognomonic signs explains the difficulty of clinical diagnosis.

Appendectomy is performed systematically. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.

But this treatment is still experimental and can be carried out peritoinw in specialized centers. Dis Colon Rectum Radiologists requested an abdominal scan to visualize an ovarian malignant pathology.

If the appendix is the most frequent origin of the disease, other tumors may be concerned for the etiology: Peritoin is a probable appendicular mucocele at the origin of this pseudomyxoma. The main sign is abdominal ascites: Should the treatment of asckte carcinomatosis by cytoreductive surgery and HIPEC still be regarded as a highly morbid procedure. J Clin Oncol The differential diagnosis includes secondary peritoneal carcinomatoses and other rare peritoneal tumors.


Ann Surg Oncol 15 5: Details and Explanations of Pathology: It presents a fine peripheral enhancement onto which enhanced tissular nodules are grafted, and there are also septa behind the left ovary and a curvilinear calcification.

Pseudomyxome péritonéal — Wikipédia

A written informed consent was obtained from the patient for the publication of this case report. Reymond ME, Solaas W.

Exploratory laparoscopy was used for diagnosis and to perform peritoneal staging, appendectomy, and ovarian biopsies. The traumatized peritoneal zones seem to favor the implantation of the mucus. CT view of abdominal scan showing that the left ovary is independent of the effusion.

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Summary and related texts. Rev Med Suisse The peritoneal lavage is then carried out. Group 4 consists of appendicular lesions of high grade, mucinous neoplasia, or invasive neoplasia invading the wall—appendicular beyond the mucous muscle.