English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.
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The etiopathogenesis of the disease remains unknown. Are you a health professional able to prescribe or dispense drugs? Continuing navigation will be considered as acceptance of this use. Diagnostic methods Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic. Many patients have been reported to have defects in blood coagulation.
Other search option s Alphabetical list. SRJ is a prestige metric ennfermedad on the idea that not all citations are the same. MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities.
Prognosis Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions. In early stages, histology of lesions may reveal a superficial and deep perivascular lymphocytic infiltration with distinct mucin deposition.
Enfermedad de Degos
From Monday to Friday from 9 a. The histology of early lesions resembles cutaneous lupus erythematosus see this term. As all patients may potentially develop the systemic, life-threatening variant, an annual follow-up is mandatory.
The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.
This condition is chronic and lesions persist over years, often throughout life. Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
In the year has been indexed in the Medlinedatabase, and has become a vehicle for expressing the most current Spanish medicine and modern. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact. Disease definition Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.
Management and treatment Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
Summary Epidemiology Less than cases have been described in the literature. It may more rarely manifest as pericarditis or in other organs such as the lungs, presenting as pleuritis. Debos, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions. More developed lesions show prominent changes in the dermoepidermal junction, with atrophy of the epidermis and an area of sclerosis in the papillary dermis.
Additional information Further information on this disease Classification s 3 Enfermmedad s 0 Clinical signs and symptoms Publications in PubMed Other website s 7. Malignant atrophic papulosis MAP is a enfeemedad, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.
This item has received. Specialised Social Services Eurordis directory. Read this article in English. Show more Show less. Genetic counseling A genetic predisposition with an autosomal dominant trait has been suggested. Previous article Next article. Later a wedge-shaped connective tissue necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs.
enfermedad de degos
Si continua navegando, consideramos que acepta su uso. Print Send to a friend Export reference Mendeley Statistics. Systemic manifestations are progressive and may lead to serious complications: Subscriber If you already have your login data, please click segos.
Subscribe to our Newsletter. Systemic lesions may affect the gastrointestinal tract and the central nervous system CNS and are potentially lethal.
Degos disease – Wikidata
To improve our services and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior. No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has been tested successfully in one case with intestinal and CNS manifestations.
Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial enfermedaf have been proposed.
Ocular involvement, which affects the eyelids, conjuctiva, retina, sclera and the choroid plexus, as well as the development of diplopia and ophthalmoplegia as secondary side effects of the neurologic involvementhas also been described. Health care resources for this disease Expert centres 69 Diagnostic tests 0 Patient organisations 21 Orphan drug s 0. Summary and related texts. Over several days, the center of the lesions sinks and develops a characteristic morphology: If you are a member of the AEDV: Etiology The etiopathogenesis of the disease remains unknown.
Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. Pemphigus Vegetans in the Inguinal Folds. Go to the members area of the website of the AEDV, https: All articles are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style. May Pages ee22 Pages The documents contained in this web site are presented for information purposes only.